发表论文
[1] Jiang, Mengying, Xu, Qiwu, Yang, Can, Li, Dan, Liu, JiWei, Zhang, Yuxian, Zhu, YongChuan, Xiong, ZhiQi. Activity-Dependent Phosphorylation of CDKL5 at Serine 407 Regulates Synaptogenesis and Plasticity. NEUROSCIENCE BULLETIN[J]. 2023, 第 8 作者 通讯作者 39(9): 1454-1458, http://sciencechina.cn/gw.jsp?action=detail.jsp&internal_id=7546608&detailType=1.[2] Xu, RuoShui, Wu, XueMei, Xiong, ZhiQi. Low-intensity ultrasound directly modulates neural activity of the cerebellar cortex. BRAIN STIMULATION[J]. 2023, 第 3 作者 通讯作者 16(3): 918-926, http://dx.doi.org/10.1016/j.brs.2023.05.012.[3] Zhu, ZiAi, Li, YiYan, Xu, Juan, Xue, Hui, Feng, Xue, Zhu, YongChuan, Xiong, ZhiQi. CDKL5 deficiency in adult glutamatergic neurons alters synaptic activity and causes spontaneous seizures via TrkB signaling. CELL REPORTS[J]. 2023, 第 7 作者 通讯作者 42(10): http://dx.doi.org/10.1016/j.celrep.2023.113202.[4] Zhai RW, Tong GY, Xiong ZQ, Wang Z. Rhesus monkeys exhibiting spontaneous ritualistic behaviors resembling obsessive-compulsive disorder.. National Science Review[J]. 2023, 10(11): [5] Min Zhao, Zijing Wang, Hang Su, Haifeng Jiang, ZhiQi Xiong, Wenlei Zhang, Jiahui Zhou, Xiaocheng Zhang, Weichen Song, Chengjie Tang, Kadir Uluda, Rongwei Zhai. Repeated methamphetamine exposure decreases plasma brain-derived neurotrophic factor levels in rhesus monkeys. GENERAL PSYCHIATRY[J]. 2023, 第 5 作者36(5): 410-416, https://doaj.org/article/fef95218a9f24d84909b6df9254b3963.[6] Zhao, M., Su, H., Zeng, Y, Sun, Y., Guo, X., Li, Y., Wang, C, Zhao, Z., Huang, X., Lin, K., Ye, Z., Lin, B., Hong, S., Zheng, J., Liu, Y., Yao, X., Yang, D., Lu, Y., Chen, H., Zuo, E., Yang, G., Wang, H., Huang, C., Lin, X., Cen, Z., Lai, L., Zhang, Y., Li, X., Lai, T., Lin, L., Zuo, D., Lin, M., Liou, C., Kong, Q., Yan, C., xiong zhiqi, Wang, N., Luo, W., Zhao, C., Cheng, X., Chen, W.. Loss of function of CMPK2 causes mitochondria deficiency and brain calcification.. Cell Discovery[J]. 2022, 第 36 作者8: 128, https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9705363/pdf/41421_2022_Article_475.pdf.[7] Lu, Bin, Lou, SenSen, Xu, RuoShui, Kong, DeLun, Wu, RongJie, Zhang, Jing, Zhuang, Ling, Wu, XueMei, He, JunYan, Wu, ZhiYing, Xiong, ZhiQi. Cerebellar spreading depolarization mediates paroxysmal movement disorder. CELL REPORTS[J]. 2021, 第 11 作者 通讯作者 36(12): http://dx.doi.org/10.1016/j.celrep.2021.109743.[8] Wang, HongTao, Zhu, ZiAi, Li, YiYan, Lou, SenSen, Yang, Guang, Feng, Xue, Xu, Wei, Huang, ZhiLi, Cheng, Xuewen, Xiong, ZhiQi. CDKL5 deficiency in forebrain glutamatergic neurons results in recurrent spontaneous seizures. EPILEPSIA[J]. 2021, 第 10 作者 通讯作者 62(2): 517-528, http://dx.doi.org/10.1111/epi.16805.[9] Wang, Fei, Wang, Qianqian, Liu, Baowei, Mei, Lisheng, Ma, Sisi, Wang, Shujuan, Wang, Ruoyu, Zhang, Yan, Niu, Chaoshi, Xiong, Zhiqi, Zheng, Yong, Zhang, Zhi, Shi, Juan, Song, Xiaoyuan. The long noncoding RNA Synage regulates synapse stability and neuronal function in the cerebellum. CELL DEATH AND DIFFERENTIATION[J]. 2021, 第 10 作者28(9): 2634-2650, http://dx.doi.org/10.1038/s41418-021-00774-3.[10] Liu, Zhen, Li, Kui, Cai, Yijun, Liu, Qiming, Zhang, Tikui, Lu, Yong, Nie, Yanhong, Wang, Yan, Yan, Zhiguang, Qu, Yinwei, Li, Yuzhuo, Wang, Zhanyang, Xiong, ZhiQi, Sun, Qiang. Accelerated passage of gene-modified monkeys by hormone-induced precocious puberty. NATIONAL SCIENCE REVIEW[J]. 2021, 第 13 作者 通讯作者 8(7): 63-66, http://sciencechina.cn/gw.jsp?action=detail.jsp&internal_id=7059495&detailType=1.[11] Xiong Zhiqi. TMEM151A variants cause paroxysmal kinesigenic dyskinesias. Cell Discovery. 2021, 第 1 作者 通讯作者 [12] Qin, XinYa, Shan, QingHong, Fang, Hui, Wang, Yu, Chen, Peng, Xiong, ZhiQi, Swaab, Dick F, Zhou, JiangNing. PSD-93 up-regulates the synaptic activity of corticotropin-releasing hormone neurons in the paraventricular nucleus in depression. ACTA NEUROPATHOLOGICA[J]. 2021, 第 6 作者142(6): 1045-1064, http://dx.doi.org/10.1007/s00401-021-02371-7.[13] WanJin Chen, Xuewen Cheng, Ying Fu, Miao Zhao, Jennifer McGinley, Ana Westenberger, ZhiQi Xiong. Rethinking monogenic neurological diseases. THE BMJ. 2020, 第 7 作者371: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7542538/.[14] Chen, WanJin, Cheng, Xuewen, Fu, Ying, Zhao, Miao, McGinley, Jennifer, Westenberger, Ana, Xiong, ZhiQi. Rethinking monogenic neurological diseases. BMJ-BRITISH MEDICAL JOURNAL[J]. 2020, 第 7 作者 通讯作者 371: http://dx.doi.org/10.1136/bmj.m3752.[15] Liu, Jianan, Pan, Limin, Shang, Chunfeng, Lu, Bin, Wu, Rongjie, Feng, Yun, Chen, Weiyu, Zhang, Rongwei, Bu, Jiwen, Xiong, Zhiqi, Bu, Wenbo, Du, Jiulin, Shi, Jianlin. A highly sensitive and selective nanosensor for near-infrared potassium imaging. SCIENCEADVANCES[J]. 2020, 第 10 作者 通讯作者 6(16): https://www.webofscience.com/wos/woscc/full-record/WOS:000528276800006.[16] Wang, Tingting, Wang, Jingyu, Wang, Jie, Mao, Lin, Tang, Bin, Vanderklish, Peter W, Liao, Xun, Xiong, ZhiQi, Liao, Lujian. HAP1 is an in vivo UBE3A target that augments autophagy in a mouse model of Angelman syndrome. NEUROBIOLOGY OF DISEASE[J]. 2019, 第 8 作者132: http://dx.doi.org/10.1016/j.nbd.2019.104585.[17] Lin, Xiang, Su, HuiZhen, Dong, EnLin, Lin, XiaoHong, Zhao, Miao, Yang, Can, Wang, Chong, Wang, Jie, Chen, YiJun, Yu, Hongjie, Xu, Jianfeng, Ma, LiXiang, Xiong, ZhiQi, Wang, Ning, Chen, WanJin. Stop-gain mutations in UBAP1 cause pure autosomal-dominant spastic paraplegia. BRAIN[J]. 2019, 第 13 作者142: 2238-2252, http://dx.doi.org/10.1093/brain/awz158.[18] Zhu, ZhiChuan, Liu, JiWei, Yang, Can, Li, MingJie, Wu, RongJie, Xiong, ZhiQi. Targeting KPNB1 overcomes TRAIL resistance by regulating DR5, Mcl-1 and FLIP in glioblastoma cells. CELL DEATH & DISEASE[J]. 2019, 第 6 作者 通讯作者 10(2): https://doaj.org/article/b3f1ac402efa455b8edd389c4f5c56d8.[19] Zhu, ZhiChuan, Liu, JiWei, Yang, Can, Zhao, Miao, Xiong, ZhiQi. XPO1 inhibitor KPT-330 synergizes with Bcl-xL inhibitor to induce cancer cell apoptosis by perturbing rRNA processing and Mcl-1 protein synthesis. CELL DEATH & DISEASE[J]. 2019, 第 5 作者 通讯作者 10(6): http://dx.doi.org/10.1038/s41419-019-1627-9.[20] Wang, Jie, Lou, SenSen, Wang, Tingting, Wu, RongJie, Li, Guangying, Zhao, Miao, Lu, Bin, Li, YiYan, Zhang, Jing, Cheng, Xuewen, Shen, Ya, Wang, Xing, Zhu, ZhiChuan, Li, MingJie, Takumi, Toru, Yang, Hui, Yu, Xiang, Liao, Lujian, Xiong, ZhiQi. UBE3A-mediated PTPA ubiquitination and degradation regulate PP2A activity and dendritic spine morphology. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA[J]. 2019, 第 19 作者 通讯作者 116(25): 12500-12505, http://dx.doi.org/10.1073/pnas.1820131116.[21] Zhu, ZhiChuan, Liu, JiWei, Li, Kui, Zheng, Jing, Xiong, ZhiQi. KPNB1 inhibition disrupts proteostasis and triggers unfolded protein response-mediated apoptosis in glioblastoma cells. ONCOGENE[J]. 2018, 第 5 作者 通讯作者 37(22): 2936-2952, http://dx.doi.org/10.1038/s41388-018-0180-9.[22] Xu, Qiong, Liu, Yuanyuan, Wang, Xiaoming, Tan, Guohe, Li, Huiping, Hulbert, Samuel W, Li, Chunyang, Hu, Chunchun, Xiong, Zhiqi, Xu, Xiu, Jiang, Yonghui. Autism-associated CHD8 deficiency impairs axon development and migration of cortical neurons. MOLECULAR AUTISM[J]. 2018, 第 9 作者9(1): https://doaj.org/article/f5e82f90f69d4bb7af33c882d69be995.[23] Xu, Xingxing, Li, Chuanyin, Gao, Xiaobo, Xia, Kun, Guo, Hui, Li, Yali, Hao, Zijian, Zhang, Lei, Gao, Daming, Xu, Chenfan, Xu, Huatai, Xiong, ZhiQi, Qiu, Zilong, Mei, Ling, Xie, Xiaoduo, Ruan, Kangcheng, Hu, Ronggui. Excessive UBE3A dosage impairs retinoic acid signaling and synaptic plasticity in autism spectrum disorders. CELL RESEARCH[J]. 2018, 第 12 作者28(1): 48-68, http://202.127.25.143/handle/331003/3402.[24] Tan, GuoHe, Liu, YuanYuan, Wang, Lu, Li, Kui, Zhang, ZeQiang, Li, HongFu, Yang, ZhongFei, Li, Yang, Li, Dan, Wu, MingYue, Yu, ChunLei, Long, JuanJuan, Chen, RenChao, Li, LiXi, Yin, LuPing, Liu, JiWei, Cheng, XueWen, Shen, Qi, Shu, YouSheng, Sakimura, Kenji, Liao, LuJian, Wu, ZhiYing, Xiong, ZhiQi. PRRT2 deficiency induces paroxysmal kinesigenic dyskinesia by regulating synaptic transmission in cerebellum. CELL RESEARCH[J]. 2018, 第 23 作者 通讯作者 28(1): 90-110, http://dx.doi.org/10.1038/cr.2017.128.[25] Yao, XiangPing, Cheng, Xuewen, Wang, Chong, Zhao, Miao, Guo, XinXin, Su, HuiZhen, Lai, LuLu, Zou, XiaoHuan, Chen, XueJiao, Zhao, Yuying, Dong, EnLin, Lu, YingQian, Wu, Shuang, Li, Xiaojuan, Fan, Gaofeng, Yu, Hongjie, Xu, Jianfeng, Wang, Ning, Xiong, ZhiQi, Chen, WanJin. Biallelic Mutations in MYORG Cause Autosomal Recessive Primary Familial Brain Calcification. NEURON[J]. 2018, 第 19 作者 通讯作者 98(6): 1116-+, http://dx.doi.org/10.1016/j.neuron.2018.05.037.[26] Yang, Zhi, Li, PengFei, Chen, RenChao, Wang, Jie, Wang, Shaoran, Shen, Ya, Wu, Xiaohui, Fang, Bing, Cheng, Xuewen, Xiong, ZhiQi. ADAM10-Initiated Release of Notch Intracellular Domain Regulates Microtubule Stability and Radial Migration of Cortical Neurons. CEREBRAL CORTEX[J]. 2017, 第 10 作者 通讯作者 27(2): 919-932, http://dx.doi.org/10.1093/cercor/bhx006.[27] Zuo, Erwei, Cai, YiJun, Li, Kui, Wei, Yu, Wang, BangAn, Sun, Yidi, Liu, Zhen, Liu, Jiwei, Hu, Xinde, Wei, Wei, Huo, Xiaona, Shi, Linyu, Tang, Cheng, Liang, Dan, Wang, Yan, Nie, YanHong, Zhang, ChenChen, Yao, Xuan, Wang, Xing, Zhou, Changyang, Ying, Wenqin, Wang, Qifang, Chen, RenChao, Shen, Qi, Xu, GuoLiang, Li, Jinsong, Sun, Qiang, Xiong, ZhiQi, Yang, Hui. One-step generation of complete gene knockout mice and monkeys by CRISPR/Cas9-mediated gene editing with multiple sgRNAs. 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Interactions Between N-Ethylmaleimide- Sensitive Factor and GluA2 Contribute to Effects of Glucocorticoid Hormones on AMPA Receptor Function in the Rodent Hippocampus. HIPPOCAMPUS[J]. 2016, 第 4 作者26(7): 848-856, https://www.webofscience.com/wos/woscc/full-record/WOS:000383272600003.[31] Li, Yang, Wang, Jie, Zhou, Yang, Li, Dan, Xiong, ZhiQi. Rcan1 Deficiency Impairs Neuronal Migration and Causes Periventricular Heterotopia. JOURNAL OF NEUROSCIENCE[J]. 2015, 第 5 作者 通讯作者 35(2): 610-620, http://ir.sibs.ac.cn/handle/331001/2668.[32] Miao, Sheng, Chen, Renchao, Ye, Jiahao, Tan, GuoHe, Li, Shuai, Zhang, Jing, Jiang, Yonghui, Xiong, ZhiQi. The Angelman Syndrome Protein Ube3a Is Required for Polarized Dendrite Morphogenesis in Pyramidal Neurons. JOURNAL OF NEUROSCIENCE[J]. 2013, 第 8 作者 通讯作者 33(1): 327-333, http://www.irgrid.ac.cn/handle/1471x/647571.[33] Li, HongFu, Ni, Wang, Xiong, ZhiQi, Xu, Jianfeng, Wu, ZhiYing. PRRT2 c.649dupC Mutation Derived from De Novo in Paroxysmal Kinesigenic Dyskinesia. CNS NEUROSCIENCE & THERAPEUTICS[J]. 2013, 第 3 作者19(1): 61-65, http://www.irgrid.ac.cn/handle/1471x/647567.[34] Lu, Tingjia, Chen, Renchao, Cox, Timothy C, Moldrich, Randal X, Kurniawan, Nyoman, Tan, Guohe, Perry, Jo K, Ashworth, Alan, Bartlett, Perry F, Xu, Li, Zhang, Jing, Lu, Bin, Wu, Mingyue, Shen, Qi, Liu, Yuanyuan, Richards, Linda J, Xiong, Zhiqi. X-linked microtubule-associated protein, Mid1, regulates axon development. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA[J]. 2013, 第 17 作者110(47): 19131-19136, http://dx.doi.org/10.1073/pnas.1303687110.[35] Zhu, YongChuan, Li, Dan, Wang, Lu, Lu, Bin, Zheng, Jing, Zhao, ShiLin, Zeng, Rong, Xiong, ZhiQi. Palmitoylation-dependent CDKL5-PSD-95 interaction regulates synaptic targeting of CDKL5 and dendritic spine development. 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EPILEPSIA[J]. 2011, 第 4 作者52(9): 1609-1616, http://www.irgrid.ac.cn/handle/1471x/502194.[39] Xiong Zhiqi. Exome sequencing identifies truncating mutations in PRRT2 that casue paroxysmal kinesigenic dyskinesia. Nature Genetics. 2011, 第 1 作者[40] Cheng, Xuewen, Li, Yang, Huang, Ying, Feng, Xiaoyan, Feng, Guoping, Xiong, ZhiQi. Pulse labeling and long-term tracing of newborn neurons in the adult subgranular zone. CELL RESEARCH[J]. 2011, 第 6 作者 通讯作者 21(2): 338-349, http://www.irgrid.ac.cn/handle/1471x/502196.[41] Hu, XiaoLing, Cheng, Xuewen, Cai, Lei, Tan, GuoHe, Xu, Li, Feng, XiaoYan, Lu, TingJia, Xiong, Hui, Fei, Jian, Xiong, ZhiQi. Conditional Deletion of NRSF in Forebrain Neurons Accelerates Epileptogenesis in the Kindling Model. CEREBRAL CORTEX[J]. 2011, 第 10 作者 通讯作者 21(9): 2158-2165, http://www.irgrid.ac.cn/handle/1471x/502195.[42] Chen, Qian, Zhu, YongChuan, Yu, Jing, Miao, Sheng, Zheng, Jing, Xu, Li, Zhou, Yang, Li, Dan, Zhang, Chi, Tao, Jiong, Xiong, ZhiQi. CDKL5, a Protein Associated with Rett Syndrome, Regulates Neuronal Morphogenesis via Rac1 Signaling. JOURNAL OF NEUROSCIENCE[J]. 2010, 第 11 作者 通讯作者 30(38): 12777-12786, http://www.irgrid.ac.cn/handle/1471x/502197.[43] Qiu, LiFeng, Lu, TingJia, Hu, XiaoLing, Yi, YongHong, Liao, WeiPing, Xiong, ZhiQi. Limbic Epileptogenesis in a Mouse Model of Fragile X Syndrome. CEREBRAL CORTEX[J]. 2009, 第 6 作者 通讯作者 19(7): 1504-1514, http://dx.doi.org/10.1093/cercor/bhn163.[44] Zhou, Yang, Lu, TingJia, Xiong, ZhiQi. NGF-dependent retrograde signaling: survival versus death. CELL RESEARCH[J]. 2009, 第 3 作者 通讯作者 19(5): 525-526, http://lib.cqvip.com/Qikan/Article/Detail?id=30274310.[45] Chen, Min, Chen, Qian, Cheng, XueWen, Lu, TingJia, Liu, HanXing, Jia, JieMin, Zhang, Chi, Xu, Li, Xiong, ZhiQi. Zn2+mediates ischemia-induced impairment of the ubiquitin-proteasome system in the rat hippocampus. JOURNAL OF NEUROCHEMISTRY[J]. 2009, 第 9 作者 通讯作者 111(5): 1094-1103, http://www.irgrid.ac.cn/handle/1471x/502198.[46] Huang, Yang Z, Pan, Enhui, Xiong, ZhiQi, McNamara, James O. Zinc-mediated transactivation of TrkB potentiates the hippocampal mossy Fiber-CA3 pyramid synapse. NEURON[J]. 2008, 第 3 作者57(4): 546-558, http://dx.doi.org/10.1016/j.neuron.2007.11.026.[47] Chen, Min, Lu, TingJia, Chen, XiaoJing, Zhou, Yang, Chen, Qian, Feng, XiaoYan, Xu, Li, Duan, WenHu, Xiong, ZhiQi. Differential Roles of NMDA Receptor Subtypes in Ischemic Neuronal Cell Death and Ischemic Tolerance. STROKE[J]. 2008, 第 9 作者 通讯作者 39(11): 3042-3048, http://ir.simm.ac.cn/handle/153631/1347.[48] Zheng, Jing, Shen, WanHua, Lu, TingJia, Zhou, Yang, Chen, Qian, Wang, Zi, Xiang, Ting, Zhu, YongChuan, Zhang, Chi, Duan, Shumin, Xiong, ZhiQi. Clathrin-dependent endocytosis is required for TrkB-dependent Akt-mediated neuronal protection and dendritic growth. 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